Zulkree Review of the literature and addition of four cases. Detailed coronal dimensions of the teeth were measured on the casts with vernier calipers, which revealed major variations in size between the teeth of the affected side compared to the uninvolved side. Ipsilateral pinna and pupil may be enlarged, but an increase in size of the inner ear or globe of the eye has not been reported [ 4 ]. This was classified by the authors as facial hemihypertrophy.
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E-mail: moc. This article has been cited by other articles in PMC. Abstract Congenital hemifacial hyperplasia CHH is a rare congenital malformation characterized by marked unilateral overdevelopment of hard and soft tissues of the face. Asymmetry in CHH is usually evident at birth and accentuated with age, especially at puberty.
The affected side grows at a rate proportional to the nonaffected side so that the disproportion is maintained thr oughout the life.
Multisystem involvement has resulted in etiological heterogeneity including heredity, chromosomal abnormalities, atypical forms of twinning, altered intrauterine environment, and endocrine dysfunctions; however, no single theory explains the etiology adequately. Deformities of all tissues of face, including teeth and their related tissues in the jaw, are key findings for correct diagnosis of CHH.
Here an attempt has been made to present a case of CHH with its archetypal features and to supplement existing clinical knowledge. Keywords: Congenital hemifacial hyperplasia, facial asymmetry, hemifacial hypertrophy Introduction Asymmetry is one of the more unusual and interesting errors of human reproduction.
Subtle, asymmetric variation of the contralateral structures of the head and face occur commonly in the general population in the absence of any local lesion or condition. Occasionally, a gross asymmetry easily perceptible to the eye may occur which progresses slowly but steadily and exhibits asymmetric development.
The purpose of this report is to present the case of a child with congenital hemifacial hyperplasia and to supplement existing clinical knowledge. He was the last of three siblings without any previous family history of facial asymmetry. The mother neither had problems during pregnancy nor during delivery.
Congenital hemifacial hyperplasia
Doujar The term hyperplasia is more precise histologically, as all tissues show an increase in the number of cells rather than an increase in cell size [ 4 ]. Occurrence of small exostoses of the posterior auditory canal has also been reported [ hsmifacial ]. The asymmetry had increased with age and ceased to grow after 18 years of age. Enlarged soft tissue mass was observed involving maxilla, mandible, and zygoma on the affected side. Unilaterally enlarged ramus, body, and condyle of mandible on the right side.
HEMIFACIAL HYPERTROPHY PDF